β-Hydroxyisovaleric Acid-d8
Cat# 469713-10mg
Size : 10mg
Brand : US Biological
469713 β-Hydroxyisovaleric Acid-d8
Clone Type
PolyclonalGrade
Highly PurifiedShipping Temp
RTStorage Temp
4°Cβ-Hydroxyisovaleric Acid-d8 is the isotope labeled analog of β-Hydroxyisovaleric Acid; a metabolite of the essential amino acid Leucine. It is synthesized in the human body and studies suggest that β-Hydroxyisovaleric Acid may have an effect on increasing muscle weight and strength. The presence of elevated β-Hydroxyisovaleric Acid is a sensitive marker of biotin deficiency and may indicate the presence of a genetic disorder such as biotinidase deficiency or holocarboxylase synthetase deficiency.||Synonyms:|3-Hydroxy-3-methylbutanoic Acid-d8; 3-Hydroxy-3-methylbutyric Acid-d8; 3-Hydroxyisovaleric Acid-d8; β-Hydroxy-β-methylbutyric Acid-d8||CAS No:|123743-99-7|Unlabeled: 625-08-1||Molecular Formula:|C₅H₂D₈O₃||Molecular Weight:|126.18||Purity:|≥97% (Isotopic)||Appearance:|Colorless to yellow oil||Solubility:|DMSO (Sparingly), Methanol (Slightly)||Method for Determining Identity:|H NMR and C NMR Spectrometric Analysis and Mass Spectrometric Analysis||TLC Conditions:|SiO2; Dichloromethane: Methanol: Acetic Acid=8:1:0.1; Visualized with AMCS; Single Spot, Rf=0.65||Normalized Intensity:|d0=0.00%, d1=0.00%, d2=0.01%, d3=0.03%, d4=0.00%, d5=0.07%, d6=0.31%, d7=4.48%, d8=95.10%||Storage and Stability:|May be stored at RT for short-term only. Long-term storage is recommended at 4ºC for 6 months after time of receipt.